Annotation Detail

Information
Associated Genes
SERPING1
Associated Variants
SERPING1 MUTATION
SERPING1 MUTATION
Associated Disease
hereditary angioedema type I
Source Database
DisGeNET
Description
SERPING1 mutations causing Hereditary Angioedema type I (HAE-I) due to C1-Inhibitor (C1-INH) deficiency display a dominant-negative effect usually resulting in protein levels far below the expected 50%.
Pubmed
25053016
Section of the abstract supporting the evidence
ALL_TEXT_1/3
Number of the section of the abstract supporting the evidence
1
Number of the sentence supporting the evidence
1
Original source reporting the Gene Disease association
BeFree,CLINVAR,ORPHANET,UNIPROT
DisGENET score for the Gene Disease association
0.360542883744161
Drugs