Annotation Detail

Information
Associated Genes
PAH
Associated Variants
PAH p.Phe39Leu (p.F39L) ( ENST00000553106.6, ENST00000307000.7 )
PAH p.Phe39Leu (p.F39L) ( ENST00000307000.7, ENST00000553106.6 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000277.3(PAH):c.117C>G (p.Phe39Leu) AND not provided
ClinVar Allele ID
15644
ClinVar RefSeq Alternation Syntax
NM_000277.3:c.117C>G
ClinVar RefSeq Alternation Syntax
NM_001354304.2:c.117C>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2024-04-01
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000078504
ClinVar Disease
not provided
Observed Origin Sample
germline
Observed Origin Sample
not provided
Drugs