Annotation Detail

Information
Associated Genes
PSEN1
Associated Variants
PSEN1 p.Ser169Pro (p.S169P) ( ENST00000700267.1, ENST00000700269.1, ENST00000556951.6, ENST00000700375.1, ENST00000553599.6, ENST00000700312.1, ENST00000700306.1, ENST00000357710.8, ENST00000700324.1, ENST00000557511.5, ENST00000700468.1, ENST00000700268.1, ENST00000700437.1, ENST00000554131.6, ENST00000700320.1, ENST00000700265.1, ENST00000700271.1, ENST00000700378.1, ENST00000394164.5, ENST00000700389.1, ENST00000700469.1, ENST00000700307.1, ENST00000557293.6, ENST00000700313.1, ENST00000700323.1, ENST00000324501.10, ENST00000700317.1, ENST00000700273.1, ENST00000700321.1, ENST00000700322.1 )
PSEN1 p.Gly206Ala (p.G206A) ( ENST00000357710.8, ENST00000700324.1, ENST00000557511.5, ENST00000700468.1, ENST00000700268.1, ENST00000700437.1, ENST00000554131.6, ENST00000700306.1, ENST00000556951.6, ENST00000700375.1, ENST00000553599.6, ENST00000700312.1, ENST00000700267.1, ENST00000700269.1, ENST00000700322.1, ENST00000324501.10, ENST00000700317.1, ENST00000700273.1, ENST00000700321.1, ENST00000557293.6, ENST00000700313.1, ENST00000700323.1, ENST00000700320.1, ENST00000700265.1, ENST00000700271.1, ENST00000700378.1, ENST00000394164.5, ENST00000700389.1, ENST00000700469.1, ENST00000700307.1 )
PSEN1 p.Gly206Val (p.G206V) ( ENST00000394164.5, ENST00000324501.10, ENST00000557511.5, ENST00000357710.8, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
STH p.Gly69Asp (p.G69D), MAPT c.1998+2821G>A ( ENST00000415613.6, ENST00000446361.7, ENST00000262410.10, ENST00000574436.5, ENST00000344290.10, ENST00000535772.6, ENST00000537309.1, ENST00000680674.1, ENST00000420682.7, ENST00000334239.12, ENST00000351559.10, ENST00000571987.5, ENST00000431008.7 )
MAPT p.Pro693Leu (p.P693L) ( ENST00000431008.7, ENST00000446361.7, ENST00000262410.10, ENST00000415613.6, ENST00000574436.5, ENST00000334239.12, ENST00000420682.7, ENST00000571987.5, ENST00000351559.10, ENST00000344290.10, ENST00000535772.6, ENST00000680674.1 )
PSEN1 p.Ser169Pro (p.S169P) ( ENST00000324501.10, ENST00000357710.8, ENST00000394164.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000557511.5, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
PSEN1 p.Gly206Ala (p.G206A) ( ENST00000324501.10, ENST00000357710.8, ENST00000394164.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000557511.5, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
PSEN1 p.Gly206Val (p.G206V) ( ENST00000324501.10, ENST00000357710.8, ENST00000394164.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000557511.5, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
STH p.Gly69Asp (p.G69D), MAPT c.1998+2821G>A ( ENST00000262410.10, ENST00000334239.12, ENST00000344290.10, ENST00000351559.10, ENST00000415613.6, ENST00000420682.7, ENST00000431008.7, ENST00000446361.7, ENST00000535772.6, ENST00000571987.5, ENST00000574436.5, ENST00000680674.1, ENST00000537309.1 )
MAPT p.Pro693Leu (p.P693L) ( ENST00000262410.10, ENST00000334239.12, ENST00000344290.10, ENST00000351559.10, ENST00000415613.6, ENST00000420682.7, ENST00000431008.7, ENST00000446361.7, ENST00000535772.6, ENST00000571987.5, ENST00000574436.5, ENST00000680674.1 )
Associated Disease
frontotemporal dementia
Source Database
DisGeNET
Description
Thirty brain regions were examined in argyrophilic grain disease (AGD; n = 5), tangle-predominant senile dementia (TPSD; n = 5), Pick disease (n = 4), familial AD (FAD; n = 2; PSEN1 p.G206A and p.S170P), and frontotemporal dementia with parkinsonism linked to chromosome-17 (FTDP-17; n = 2; MAPT p.P301L and IVS10 + 16).
Pubmed
23885714
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.369077133910489
Year of publication
2013
Drugs