Annotation Detail

Information
Associated Genes
SCN5A
Associated Variants
SCN5A p.Tyr1795Cys (p.Y1795C) ( ENST00000333535.9, ENST00000450102.6, ENST00000455624.6, ENST00000449557.6, ENST00000414099.6, ENST00000423572.7, ENST00000413689.6 )
SCN5A p.Tyr1795Cys (p.Y1795C) ( ENST00000333535.9, ENST00000413689.6, ENST00000414099.6, ENST00000423572.7, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
Associated Disease
long QT syndrome
Source Database
DisGeNET
Description
Interestingly another LQT-3 mutant (Y1795C) shows no change in flecainide sensitivity, suggesting that although drug effects of SCN5A mutations cross disease boundaries, clinical management with flecainide will be beneficial to patients in a mutation-specific manner.
Pubmed
12814325
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.334978501186199
Year of publication
2003
Drugs