Annotation Detail

Information
Associated Genes
SCN5A
Associated Variants
SCN5A p.Tyr1795Cys (p.Y1795C) ( ENST00000333535.9, ENST00000450102.6, ENST00000455624.6, ENST00000449557.6, ENST00000414099.6, ENST00000423572.7, ENST00000413689.6 )
SCN5A p.Tyr1795His (p.Y1795H) ( ENST00000333535.9, ENST00000413689.6, ENST00000414099.6, ENST00000423572.7, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
SCN5A p.Tyr1795Cys (p.Y1795C) ( ENST00000333535.9, ENST00000413689.6, ENST00000414099.6, ENST00000423572.7, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
SCN5A p.Tyr1795His (p.Y1795H) ( ENST00000333535.9, ENST00000413689.6, ENST00000414099.6, ENST00000423572.7, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
Associated Disease
long QT syndrome
Source Database
DisGeNET
Description
Recently, two novel missense mutations at the same codon in the gene encoding the cardiac Na+ channel (SCN5A) have been identified: Y1795C (causing the LQTS phenotype) and Y1795H (causing the BrS phenotype).
Pubmed
16929919
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.334978501186199
Year of publication
2006
Drugs