Annotation Detail

Information
Associated Genes
DARS2
Associated Variants
DARS2 p.Ser45Gly (p.S45G) ( ENST00000649689.2, ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1 )
DARS2 p.Cys152Phe (p.C152F) ( ENST00000649689.2, ENST00000648458.1, ENST00000648807.1, ENST00000647645.1, ENST00000649067.1, ENST00000648960.1 )
DARS2 c.492+2T>C ( ENST00000649689.2, ENST00000648458.1, ENST00000648807.1, ENST00000647645.1, ENST00000649067.1, ENST00000648960.1 )
DARS2 c.492+2T>G ( ENST00000649067.1, ENST00000648960.1, ENST00000648458.1, ENST00000648807.1, ENST00000647645.1, ENST00000649689.2 )
DARS2 p.Arg179His (p.R179H) ( ENST00000649689.2, ENST00000648960.1, ENST00000649067.1, ENST00000647645.1, ENST00000648458.1, ENST00000648807.1 )
DARS2 p.Arg263Ter (p.R263*) ( ENST00000649689.2, ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1 )
DARS2 p.Arg263Gln (p.R263Q) ( ENST00000649689.2, ENST00000648458.1, ENST00000648807.1, ENST00000647645.1, ENST00000649067.1, ENST00000648960.1 )
DARS2 p.Arg263Pro (p.R263P) ( ENST00000648960.1, ENST00000649067.1, ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000649689.2 )
DARS2 p.Glu425Ter (p.E425*) ( ENST00000649689.2, ENST00000649067.1, ENST00000648960.1, ENST00000648458.1, ENST00000648807.1, ENST00000647645.1 )
DARS2 p.Arg609Trp (p.R609W) ( ENST00000649689.2, ENST00000649067.1, ENST00000648960.1, ENST00000648807.1, ENST00000647645.1 )
DARS2 p.Leu613Phe (p.L613F) ( ENST00000649689.2, ENST00000649067.1, ENST00000648960.1, ENST00000648807.1, ENST00000647645.1 )
DARS2 p.Leu626Val (p.L626V) ( ENST00000649689.2, ENST00000648960.1, ENST00000649067.1, ENST00000647645.1, ENST00000648807.1 )
DARS2 p.Leu626Gln (p.L626Q) ( ENST00000648807.1, ENST00000647645.1, ENST00000649067.1, ENST00000648960.1, ENST00000649689.2 )
DARS2 p.Ser45Gly (p.S45G) ( ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Cys152Phe (p.C152F) ( ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 c.492+2T>C ( ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 c.492+2T>G ( ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Arg179His (p.R179H) ( ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Arg263Ter (p.R263*) ( ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Arg263Gln (p.R263Q) ( ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Arg263Pro (p.R263P) ( ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Glu425Ter (p.E425*) ( ENST00000647645.1, ENST00000648458.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Arg609Trp (p.R609W) ( ENST00000647645.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Leu613Phe (p.L613F) ( ENST00000647645.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Leu626Val (p.L626V) ( ENST00000647645.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 p.Leu626Gln (p.L626Q) ( ENST00000647645.1, ENST00000648807.1, ENST00000648960.1, ENST00000649067.1, ENST00000649689.2 )
DARS2 c.228-22_228-21insC
DARS2 c.228-22_228-21insCC
DARS2 c.228-20_228-19insTT
DARS2 c.228-22_228-21insC
DARS2 c.228-22_228-21insCC
DARS2 c.228-20_228-19insTT
Associated Disease
Leukoencephalopathy with Brainstem and Spinal Cord Involvement and Lactate Elevation
Source Database
DisGeNET
Description
NA
Original source reporting the Gene Disease association
CLINVAR
DisGENET score for the Gene Disease association
0.480542883744161
Year of publication
NA
Drugs