Annotation Detail

Information
Associated Genes
KCNQ1
Associated Variants
KCNQ1 p.Thr587Met (p.T587M) ( ENST00000526095.2, ENST00000335475.6, ENST00000155840.12, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
KCNQ1 p.Thr587Met (p.T587M) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000526095.2, ENST00000646564.2, ENST00000713725.1 )
Associated Disease
long QT syndrome
Source Database
DisGeNET
Description
Trafficking-deficient long QT syndrome mutation KCNQ1-T587M confers severe clinical phenotype by impairment of KCNH2 membrane localization: evidence for clinically significant IKr-IKs alpha-subunit interaction.
Pubmed
19959132
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.41651083741347
Year of publication
2009
Drugs