Annotation Detail

Information
Associated Genes
KCNQ1
Associated Variants
KCNQ1 p.Val254Met (p.V254M) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
KCNQ1 p.Val254Leu (p.V254L) ( ENST00000646564.2, ENST00000335475.6, ENST00000713725.1, ENST00000496887.7, ENST00000155840.12 )
KCNQ1 p.Val254Leu (p.V254L) ( ENST00000496887.7, ENST00000155840.12, ENST00000713725.1, ENST00000335475.6, ENST00000646564.2 )
KCNQ1 p.Val254Met (p.V254M) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
KCNQ1 p.Val254Leu (p.V254L) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
KCNQ1 p.Val254Leu (p.V254L) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
Associated Disease
long QT syndrome
Source Database
DisGeNET
Description
The second mutation, V254M in KCNQ1, co-segregated with higher QT intervals and symptoms in other family members, and was previously reported in another LQTS family.
Pubmed
12820704
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.41651083741347
Year of publication
2003
Drugs