Annotation Detail

Information
Associated Genes
SMPD1
Associated Variants
SMPD1 p.Trp393Gly (p.W393G) ( ENST00000342245.9, ENST00000527275.5 )
SMPD1 p.Trp393Gly (p.W393G) ( ENST00000342245.9, ENST00000527275.5 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000543.5(SMPD1):c.1177T>G (p.Trp393Gly) AND not provided
ClinVar Allele ID
18030
ClinVar RefSeq Alternation Syntax
NM_001365135.2:c.1132-316T>G
ClinVar RefSeq Alternation Syntax
NM_000543.5:c.1177T>G
ClinVar RefSeq Alternation Syntax
NM_001318087.2:c.1177T>G
ClinVar RefSeq Alternation Syntax
NM_001318088.2:c.256T>G
ClinVar RefSeq Alternation Syntax
NM_001007593.3:c.1174T>G
ClinVar RefSeq Alternation Syntax
NR_134502.2:n.649T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2024-04-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV004546410
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs