Annotation Detail

Information
Associated Genes
KCNJ11
Associated Variants
KCNJ11 p.Val252Ala (p.V252A) ( ENST00000339994.5, ENST00000682764.1, ENST00000682350.1, ENST00000528731.1 )
KCNJ11 p.Val252Ala (p.V252A) ( ENST00000339994.5, ENST00000528731.1, ENST00000682350.1, ENST00000682764.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000525.4(KCNJ11):c.755T>C (p.Val252Ala) AND not provided
ClinVar Allele ID
34052
ClinVar RefSeq Alternation Syntax
NM_000525.4:c.755T>C
ClinVar RefSeq Alternation Syntax
NM_001377297.1:c.494T>C
ClinVar RefSeq Alternation Syntax
NM_001377296.1:c.494T>C
ClinVar RefSeq Alternation Syntax
NM_001166290.2:c.494T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-08-08
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003556057
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs