Annotation Detail

Information
Associated Genes
PDGFRA
Associated Variants
PDGFRA p.Thr674Ile (p.T674I), ENSG00000282278 p.Thr434Ile (p.T434I) ( ENST00000257290.10 )
PDGFRA p.Thr674Ile (p.T674I), ENSG00000282278 p.Thr434Ile (p.T434I) ( ENST00000257290.10 )
Associated Disease
gastrointestinal stromal tumor
Source Database
ClinVar
Description
NM_006206.6(PDGFRA):c.2021C>T (p.Thr674Ile) AND Gastrointestinal stromal tumor
ClinVar Allele ID
28589
ClinVar RefSeq Alternation Syntax
NM_006206.6:c.2021C>T
ClinVar RefSeq Alternation Syntax
NM_001347827.2:c.2021C>T
ClinVar RefSeq Alternation Syntax
NM_001347830.2:c.2060C>T
ClinVar RefSeq Alternation Syntax
NM_001347829.2:c.2021C>T
ClinVar RefSeq Alternation Syntax
NM_001347828.2:c.2096C>T
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2023-09-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003525857
ClinVar Disease
Gastrointestinal stromal tumor
Observed Origin Sample
germline
Drugs