Annotation Detail

Information
Associated Genes
ATM
Associated Variants
ATM p.Ser47Ter (p.S47*) ( ENST00000639953.1, ENST00000640388.1, ENST00000683914.2, ENST00000601453.3, ENST00000713847.1, ENST00000531525.3, ENST00000713846.1, ENST00000683150.1, ENST00000682465.1, ENST00000684029.1, ENST00000278616.10, ENST00000452508.7, ENST00000675843.1, ENST00000683468.1, ENST00000639240.1, ENST00000713845.1, ENST00000526567.5, ENST00000713844.1, ENST00000532931.6, ENST00000530958.5 )
ATM p.Ser47Ter (p.S47*) ( ENST00000682465.1, ENST00000683150.1, ENST00000683468.1, ENST00000683914.2, ENST00000684029.1, ENST00000713844.1, ENST00000713845.1, ENST00000713846.1, ENST00000713847.1, ENST00000278616.10, ENST00000452508.7, ENST00000526567.5, ENST00000530958.5, ENST00000531525.3, ENST00000532931.6, ENST00000601453.3, ENST00000639240.1, ENST00000639953.1, ENST00000640388.1, ENST00000675843.1 )
Associated Disease
Familial cancer of breast
Source Database
ClinVar
Description
NM_000051.4(ATM):c.140C>G (p.Ser47Ter) AND Familial cancer of breast
ClinVar Allele ID
212835
ClinVar RefSeq Alternation Syntax
NM_001351835.2:c.140C>G
ClinVar RefSeq Alternation Syntax
NM_000051.4:c.140C>G
ClinVar RefSeq Alternation Syntax
NM_001351836.2:c.140C>G
ClinVar RefSeq Alternation Syntax
NM_001351834.2:c.140C>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-10-11
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003454496
ClinVar Disease
Familial cancer of breast
Observed Origin Sample
unknown
Drugs