Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Leu2241Val (p.L2241V) ( ENST00000370225.4 )
ABCA4 p.Leu2241Val (p.L2241V) ( ENST00000370225.4 )
Associated Disease
Stargardt disease
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.6721C>G (p.Leu2241Val) AND Stargardt disease
ClinVar Allele ID
105376
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.6499C>G
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.6721C>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2023-07-24
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003324515
ClinVar Disease
Stargardt disease
Observed Origin Sample
germline
Drugs