Annotation Detail

Information
Associated Genes
TERT
Associated Variants
TERT p.Thr726Met (p.T726M) ( ENST00000310581.10, ENST00000334602.10 )
TERT p.Thr726Met (p.T726M) ( ENST00000310581.10, ENST00000334602.10 )
Associated Disease
Idiopathic Pulmonary Fibrosis Dyskeratosis congenita, autosomal dominant 2
Source Database
ClinVar
Description
NM_198253.3(TERT):c.2177C>T (p.Thr726Met) AND multiple conditions
ClinVar Allele ID
47717
ClinVar RefSeq Alternation Syntax
NM_198253.3:c.2177C>T
ClinVar RefSeq Alternation Syntax
NM_001193376.3:c.2177C>T
ClinVar RefSeq Alternation Syntax
NR_149162.3:n.2256C>T
ClinVar RefSeq Alternation Syntax
NR_149163.3:n.2220C>T
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2024-01-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002514133
ClinVar Disease
Idiopathic Pulmonary Fibrosis
ClinVar Disease
Dyskeratosis congenita, autosomal dominant 2
Observed Origin Sample
germline
Drugs