Annotation Detail

Information
Associated Genes
TERT LOC110806263
Associated Variants
TERT c.219+1G>A ( ENST00000310581.10, ENST00000334602.10 )
TERT c.219+1G>A ( ENST00000310581.10, ENST00000334602.10 )
Associated Disease
Dyskeratosis congenita, autosomal dominant 2 Idiopathic Pulmonary Fibrosis
Source Database
ClinVar
Description
NM_198253.3(TERT):c.219+1G>A AND multiple conditions
ClinVar Allele ID
27777
ClinVar RefSeq Alternation Syntax
NM_001193376.3:c.219+1G>A
ClinVar RefSeq Alternation Syntax
NM_198253.3:c.219+1G>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2021-08-04
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002513017
ClinVar Disease
Idiopathic Pulmonary Fibrosis
ClinVar Disease
Dyskeratosis congenita, autosomal dominant 2
Observed Origin Sample
germline
Drugs