Annotation Detail

Information
Associated Genes
BRCA2
Associated Variants
BRCA2 p.Arg2336His (p.R2336H) ( ENST00000380152.8, ENST00000530893.7, ENST00000544455.6, ENST00000700202.2, ENST00000713678.1, ENST00000713680.1 )
BRCA2 p.Arg2336His (p.R2336H) ( ENST00000380152.8, ENST00000530893.7, ENST00000544455.6, ENST00000700202.2, ENST00000713678.1, ENST00000713680.1 )
Associated Disease
Wilms tumor 1 Familial cancer of breast Pancreatic cancer, susceptibility to, 2 Fanconi anemia complementation group D1 Breast-ovarian cancer, familial, susceptibility to, 2 Glioma susceptibility 3 medulloblastoma Malignant tumor of prostate
Source Database
ClinVar
Description
NM_000059.4(BRCA2):c.7007G>A (p.Arg2336His) AND multiple conditions
ClinVar Allele ID
46633
ClinVar RefSeq Alternation Syntax
NM_000059.4:c.7007G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-10-07
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002496486
ClinVar Disease
Fanconi anemia complementation group D1
ClinVar Disease
Malignant tumor of prostate
ClinVar Disease
Medulloblastoma
ClinVar Disease
Wilms tumor 1
ClinVar Disease
Breast-ovarian cancer, familial, susceptibility to, 2
ClinVar Disease
Familial cancer of breast
ClinVar Disease
Pancreatic cancer, susceptibility to, 2
ClinVar Disease
Glioma susceptibility 3
Observed Origin Sample
unknown
Drugs