Annotation Detail

Information
Associated Genes
SLC2A1
Associated Variants
SLC2A1 p.Arg92Trp (p.R92W) ( ENST00000426263.10, ENST00000674765.1 )
SLC2A1 p.Arg92Trp (p.R92W) ( ENST00000426263.10, ENST00000674765.1 )
Associated Disease
Childhood onset GLUT1 deficiency syndrome 2 Encephalopathy due to GLUT1 deficiency
Source Database
ClinVar
Description
NM_006516.4(SLC2A1):c.274C>T (p.Arg92Trp) AND multiple conditions
ClinVar Allele ID
31158
ClinVar RefSeq Alternation Syntax
NM_006516.4:c.274C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-05-13
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002243647
ClinVar Disease
Encephalopathy due to GLUT1 deficiency
ClinVar Disease
Childhood onset GLUT1 deficiency syndrome 2
Observed Origin Sample
de novo
Drugs