Annotation Detail

Information
Associated Genes
HJV
Associated Variants
HJV p.Cys80Arg (p.C80R) ( ENST00000636675.1, ENST00000475797.1, ENST00000336751.11, ENST00000497365.5, ENST00000357836.5, ENST00000634927.1 )
HJV p.Cys80Arg (p.C80R) ( ENST00000336751.11, ENST00000357836.5, ENST00000475797.1, ENST00000497365.5, ENST00000634927.1, ENST00000636675.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_213653.4(HJV):c.238T>C (p.Cys80Arg) AND not provided
ClinVar Allele ID
17408
ClinVar RefSeq Alternation Syntax
NM_213652.4:c.-21-894T>C
ClinVar RefSeq Alternation Syntax
NM_213653.4:c.238T>C
ClinVar RefSeq Alternation Syntax
NM_145277.5:c.-102T>C
ClinVar RefSeq Alternation Syntax
NM_202004.4:c.-22+104T>C
ClinVar RefSeq Alternation Syntax
NM_001316767.2:c.-22+104T>C
ClinVar RefSeq Alternation Syntax
NM_001379352.1:c.238T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-12-11
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001851583
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs