Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Tyr136Ter (p.Y136*) ( ENST00000382848.5, ENST00000382844.2 )
GJB2 p.Tyr136Ter (p.Y136*) ( ENST00000382848.5, ENST00000382844.2 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_004004.6(GJB2):c.408C>A (p.Tyr136Ter) AND not provided
ClinVar Allele ID
186856
ClinVar RefSeq Alternation Syntax
NM_004004.6:c.408C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-11-28
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001850402
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs