Annotation Detail

Information
Associated Genes
PRNP
Associated Variants
PRNP p.Arg208His (p.R208H) ( ENST00000379440.9, ENST00000424424.2, ENST00000430350.2, ENST00000457586.2 )
PRNP p.Arg208His (p.R208H) ( ENST00000379440.9, ENST00000424424.2, ENST00000430350.2, ENST00000457586.2 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000311.5(PRNP):c.623G>A (p.Arg208His) AND not provided
ClinVar Allele ID
28450
ClinVar RefSeq Alternation Syntax
NM_000311.5:c.623G>A
ClinVar RefSeq Alternation Syntax
NM_001080122.3:c.623G>A
ClinVar RefSeq Alternation Syntax
NM_001080121.3:c.623G>A
ClinVar RefSeq Alternation Syntax
NM_001271561.3:c.*312G>A
ClinVar RefSeq Alternation Syntax
NM_001080123.3:c.623G>A
ClinVar RefSeq Alternation Syntax
NM_183079.4:c.623G>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2023-03-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001823096
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs