Annotation Detail

Information
Associated Genes
SCN5A
Associated Variants
SCN5A p.Arg1623Gln (p.R1623Q) ( ENST00000423572.7, ENST00000413689.6, ENST00000333535.9, ENST00000414099.6, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
SCN5A p.Arg1623Gln (p.R1623Q) ( ENST00000333535.9, ENST00000413689.6, ENST00000414099.6, ENST00000423572.7, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000335.5(SCN5A):c.4865G>A (p.Arg1622Gln) AND not provided
ClinVar Allele ID
24415
ClinVar RefSeq Alternation Syntax
NM_001099405.2:c.4814G>A
ClinVar RefSeq Alternation Syntax
NM_001160161.2:c.4706G>A
ClinVar RefSeq Alternation Syntax
NM_001160160.2:c.4769G>A
ClinVar RefSeq Alternation Syntax
NM_001354701.2:c.4811G>A
ClinVar RefSeq Alternation Syntax
NM_198056.3:c.4868G>A
ClinVar RefSeq Alternation Syntax
NM_001099404.2:c.4868G>A
ClinVar RefSeq Alternation Syntax
NM_000335.5:c.4865G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-04-25
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001588806
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs