Annotation Detail

Information
Associated Genes
ADA
Associated Variants
ADA p.Arg156Cys (p.R156C) ( ENST00000537820.2, ENST00000536076.2, ENST00000372874.9, ENST00000696078.1, ENST00000695889.1, ENST00000695927.1, ENST00000695949.1, ENST00000695991.1, ENST00000695993.1, ENST00000695995.1, ENST00000696017.1, ENST00000696058.1, ENST00000696060.1, ENST00000696061.1, ENST00000696062.1, ENST00000696063.1, ENST00000696064.1, ENST00000696065.1, ENST00000696076.1, ENST00000696077.1, ENST00000696079.1, ENST00000696080.1, ENST00000696082.1 )
ADA p.Arg156Cys (p.R156C) ( ENST00000696060.1, ENST00000695949.1, ENST00000696061.1, ENST00000696062.1, ENST00000695995.1, ENST00000696063.1, ENST00000696064.1, ENST00000696065.1, ENST00000696076.1, ENST00000696077.1, ENST00000696078.1, ENST00000372874.9, ENST00000696080.1, ENST00000696082.1, ENST00000695927.1, ENST00000695993.1, ENST00000695889.1, ENST00000537820.2, ENST00000536076.2, ENST00000695991.1, ENST00000696058.1, ENST00000696017.1, ENST00000696079.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000022.4(ADA):c.466C>T (p.Arg156Cys) AND not provided
ClinVar Allele ID
17009
ClinVar RefSeq Alternation Syntax
NM_001322051.2:c.466C>T
ClinVar RefSeq Alternation Syntax
NM_001322050.2:c.73+875C>T
ClinVar RefSeq Alternation Syntax
NM_000022.4:c.466C>T
ClinVar RefSeq Alternation Syntax
NR_136160.2:n.558C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-05-19
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001588796
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs