Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Arg200Trp (p.R200W) ( ENST00000541395.5, ENST00000544413.2, ENST00000257555.11, ENST00000400024.6 )
HNF1A p.Arg200Trp (p.R200W) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000545.5(HNF1A):c.598C>T (p.Arg200Trp) AND not provided
ClinVar Allele ID
45485
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.598C>T
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.598C>T
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2023-08-23
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001570589
ClinVar Disease
not provided
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs