Annotation Detail

Information
Associated Genes
ADAMTS13
Associated Variants
ADAMTS13 p.Thr196Ile (p.T196I) ( ENST00000355699.7, ENST00000356589.6, ENST00000371911.7, ENST00000371916.5, ENST00000371929.7 )
ADAMTS13 p.Thr196Ile (p.T196I) ( ENST00000355699.7, ENST00000356589.6, ENST00000371911.7, ENST00000371916.5, ENST00000371929.7 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_139027.6(ADAMTS13):c.587C>T (p.Thr196Ile) AND not provided
ClinVar Allele ID
20840
ClinVar RefSeq Alternation Syntax
NM_139025.5:c.587C>T
ClinVar RefSeq Alternation Syntax
NM_139027.6:c.587C>T
ClinVar RefSeq Alternation Syntax
NM_139026.6:c.587C>T
ClinVar RefSeq Alternation Syntax
NR_024514.3:n.790C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-10-25
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001507764
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs