Annotation Detail

Information
Associated Genes
VHL LOC107303340
Associated Variants
VHL p.Thr157Ile (p.T157I) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
VHL p.Thr157Ile (p.T157I) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000551.4(VHL):c.470C>T (p.Thr157Ile) AND not provided
ClinVar Allele ID
224953
ClinVar RefSeq Alternation Syntax
NM_001354723.2:c.*24C>T
ClinVar RefSeq Alternation Syntax
NM_198156.3:c.347C>T
ClinVar RefSeq Alternation Syntax
NM_000551.4:c.470C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-11-29
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001289415
ClinVar Disease
not provided
Observed Origin Sample
unknown
Drugs