Annotation Detail

Information
Associated Genes
HJV
Associated Variants
HJV p.Arg326Ter (p.R326*) ( ENST00000636675.1, ENST00000336751.11, ENST00000475797.1, ENST00000357836.5, ENST00000497365.5 )
HJV p.Arg326Ter (p.R326*) ( ENST00000336751.11, ENST00000357836.5, ENST00000475797.1, ENST00000497365.5, ENST00000636675.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_213653.4(HJV):c.976C>T (p.Arg326Ter) AND not provided
ClinVar Allele ID
17405
ClinVar RefSeq Alternation Syntax
NM_202004.4:c.298C>T
ClinVar RefSeq Alternation Syntax
NM_145277.5:c.637C>T
ClinVar RefSeq Alternation Syntax
NM_213653.4:c.976C>T
ClinVar RefSeq Alternation Syntax
NM_001316767.2:c.298C>T
ClinVar RefSeq Alternation Syntax
NM_213652.4:c.298C>T
ClinVar RefSeq Alternation Syntax
NM_001379352.1:c.976C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-12-18
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001216451
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs