Annotation Detail

Information
Associated Genes
PRNP
Associated Variants
PRNP p.Asp178Asn (p.D178N) ( ENST00000430350.2, ENST00000457586.2, ENST00000424424.2, ENST00000379440.9 )
PRNP p.Asp178Asn (p.D178N) ( ENST00000424424.2, ENST00000379440.9, ENST00000457586.2, ENST00000430350.2 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000311.5(PRNP):c.532G>A (p.Asp178Asn) AND not provided
ClinVar Allele ID
28438
ClinVar RefSeq Alternation Syntax
NM_001080123.3:c.532G>A
ClinVar RefSeq Alternation Syntax
NM_183079.4:c.532G>A
ClinVar RefSeq Alternation Syntax
NM_001080122.3:c.532G>A
ClinVar RefSeq Alternation Syntax
NM_000311.5:c.532G>A
ClinVar RefSeq Alternation Syntax
NM_001080121.3:c.532G>A
ClinVar RefSeq Alternation Syntax
NM_001271561.3:c.*221G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-03-01
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001200144
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs