Annotation Detail

Information
Associated Genes
VPS13C
Associated Variants
VPS13C p.Arg3652Ter (p.R3652*) ( ENST00000644861.2, ENST00000249837.7 )
VPS13C p.Arg3652Ter (p.R3652*) ( ENST00000249837.7, ENST00000644861.2 )
Associated Disease
frontotemporal dementia Primary degenerative dementia of the Alzheimer type, presenile onset
Source Database
ClinVar
Description
NM_020821.3(VPS13C):c.10954C>T (p.Arg3652Ter) AND multiple conditions
ClinVar Allele ID
858707
ClinVar RefSeq Alternation Syntax
NM_020821.3:c.10954C>T
ClinVar RefSeq Alternation Syntax
NM_017684.5:c.10825C>T
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2019-10-28
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001090104
ClinVar Disease
Primary degenerative dementia of the Alzheimer type, presenile onset
ClinVar Disease
Frontotemporal dementia
Observed Origin Sample
unknown
Drugs