Annotation Detail

Information
Associated Genes
ARSA
Associated Variants
ARSA p.Arg86Trp (p.R86W) ( ENST00000216124.10, ENST00000356098.9, ENST00000395619.3, ENST00000395621.7, ENST00000453344.6 )
ARSA p.Arg86Trp (p.R86W) ( ENST00000216124.10, ENST00000356098.9, ENST00000395619.3, ENST00000395621.7, ENST00000453344.6 )
Associated Disease
frontotemporal dementia
Source Database
ClinVar
Description
NM_000487.6(ARSA):c.256C>T (p.Arg86Trp) AND Frontotemporal dementia
ClinVar Allele ID
79017
ClinVar RefSeq Alternation Syntax
NM_001362782.2:c.-3C>T
ClinVar RefSeq Alternation Syntax
NM_001085425.3:c.256C>T
ClinVar RefSeq Alternation Syntax
NM_000487.6:c.256C>T
ClinVar RefSeq Alternation Syntax
NM_001085426.3:c.256C>T
ClinVar RefSeq Alternation Syntax
NM_001085427.3:c.256C>T
ClinVar RefSeq Alternation Syntax
NM_001085428.3:c.-3C>T
Clinical Significance Description
no classifications from unflagged records
Clinical Significance Last Update
2024-02-19
Clinical Significance Review Status
no classifications from unflagged records
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001090098
ClinVar Disease
Frontotemporal dementia
Observed Origin Sample
unknown
Drugs