Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Arg1898His (p.R1898H) ( ENST00000370225.4 )
ABCA4 p.Glu471Lys (p.E471K) ( ENST00000649773.1, ENST00000370225.4 )
ABCA4 p.Arg1898His (p.R1898H) ( ENST00000370225.4 )
ABCA4 p.Glu471Lys (p.E471K) ( ENST00000370225.4, ENST00000649773.1 )
Associated Disease
retinitis pigmentosa
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.[1411G>A;5693G>A] AND Retinitis pigmentosa
ClinVar Allele ID
105287
ClinVar Allele ID
104942
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.1411G>A
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.5693G>A
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.5471G>A
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.1411G>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2019-06-23
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001002804
ClinVar Disease
Retinitis pigmentosa
Observed Origin Sample
inherited
Drugs