Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Gly863Ala (p.G863A) ( ENST00000370225.4, ENST00000649773.1 )
ABCA4 p.Gly863Ala (p.G863A) ( ENST00000370225.4, ENST00000649773.1 )
Associated Disease
Stargardt disease
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.2588G>C (p.Gly863Ala) AND Stargardt disease
ClinVar Allele ID
22918
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.2588G>C
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.2366G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-08-24
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000787486
ClinVar Disease
Stargardt disease
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs