Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Gly1961Glu (p.G1961E) ( ENST00000370225.4 )
ABCA4 p.His1838Asp (p.H1838D) ( ENST00000370225.4 )
ABCA4 p.Gly1961Glu (p.G1961E) ( ENST00000370225.4 )
ABCA4 p.His1838Asp (p.H1838D) ( ENST00000370225.4 )
Associated Disease
Stargardt disease
Source Database
ClinVar
Description
NM_000350.2(ABCA4):c.[5512C>G;5882G>A] AND Stargardt disease
ClinVar Allele ID
105269
ClinVar Allele ID
22927
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.5512C>G
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.5660G>A
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.5290C>G
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.5882G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-12-13
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000786006
ClinVar Disease
Stargardt disease
Observed Origin Sample
inherited
Drugs