Annotation Detail

Information
Associated Genes
ADAMTS13
Associated Variants
ADAMTS13 p.Pro475Ser (p.P475S) ( ENST00000355699.7, ENST00000356589.6, ENST00000371916.5, ENST00000371929.7 )
ADAMTS13 p.Pro475Ser (p.P475S) ( ENST00000355699.7, ENST00000356589.6, ENST00000371916.5, ENST00000371929.7 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_139027.6(ADAMTS13):c.1423C>T (p.Pro475Ser) AND not provided
ClinVar Allele ID
20853
ClinVar RefSeq Alternation Syntax
NM_139025.5:c.1423C>T
ClinVar RefSeq Alternation Syntax
NM_139027.6:c.1423C>T
ClinVar RefSeq Alternation Syntax
NM_139026.6:c.1330C>T
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2024-01-22
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000767050
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs