Annotation Detail

Information
Associated Genes
RB1
Associated Variants
RB1 p.Arg661Trp (p.R661W) ( ENST00000267163.6, ENST00000650461.1, ENST00000713856.1, ENST00000713857.1, ENST00000713858.1 )
RB1 p.Arg661Trp (p.R661W) ( ENST00000267163.6, ENST00000650461.1, ENST00000713856.1, ENST00000713857.1, ENST00000713858.1 )
Associated Disease
Small cell lung carcinoma Malignant tumor of urinary bladder retinoblastoma bone osteosarcoma
Source Database
ClinVar
Description
NM_000321.3(RB1):c.1981C>T (p.Arg661Trp) AND multiple conditions
ClinVar Allele ID
28126
ClinVar RefSeq Alternation Syntax
NM_000321.3:c.1981C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2018-10-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000763335
ClinVar Disease
Bone osteosarcoma
ClinVar Disease
Malignant tumor of urinary bladder
ClinVar Disease
Small cell lung carcinoma
ClinVar Disease
Retinoblastoma
Observed Origin Sample
unknown
Drugs