Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB p.Arg46Ter (p.R46*) ( ENST00000549165.1, ENST00000392919.4, ENST00000549940.5, ENST00000299314.12 )
GNPTAB p.Arg46Ter (p.R46*) ( ENST00000299314.12, ENST00000392919.4, ENST00000549165.1, ENST00000549940.5 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_024312.5(GNPTAB):c.136C>T (p.Arg46Ter) AND not provided
ClinVar Allele ID
47634
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.136C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-09-17
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000760392
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs