Annotation Detail

Information
Associated Genes
POLR2F SOX10
Associated Variants
SOX10 p.Gln377Ter (p.Q377*), POLR2F c.293+6597G>A ( ENST00000407936.5, ENST00000360880.6, ENST00000405557.5, ENST00000698177.1, ENST00000396884.8 )
SOX10 p.Gln377Ter (p.Q377*), POLR2F c.293+6597G>A ( ENST00000405557.5, ENST00000407936.5, ENST00000396884.8, ENST00000698177.1, ENST00000360880.6 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_006941.4(SOX10):c.1129C>T (p.Gln377Ter) AND not provided
ClinVar Allele ID
22441
ClinVar RefSeq Alternation Syntax
NM_001363825.1:c.*38+1457G>A
ClinVar RefSeq Alternation Syntax
NM_006941.4:c.1129C>T
ClinVar RefSeq Alternation Syntax
NM_001301131.2:c.293+6597G>A
ClinVar RefSeq Alternation Syntax
NM_001301130.2:c.293+6597G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-01-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000760372
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs