Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Val198GlnfsTer4 (p.V198Qfs*4) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Val198GlnfsTer4 (p.V198Qfs*4) ( ENST00000382844.2, ENST00000382848.5 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_004004.6(GJB2):c.592_600delinsCAGTGTTCATGACATTC (p.Val198_Gly200delinsGlnCysSerTer) AND not provided
ClinVar Allele ID
53928
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-09-08
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000727541
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs