Annotation Detail

Information
Associated Genes
ARSA
Associated Variants
ARSA p.Arg86Gln (p.R86Q) ( ENST00000216124.10, ENST00000356098.9, ENST00000395619.3, ENST00000395621.7, ENST00000453344.6 )
ARSA p.Arg86Gln (p.R86Q) ( ENST00000216124.10, ENST00000356098.9, ENST00000395619.3, ENST00000395621.7, ENST00000453344.6 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000487.6(ARSA):c.257G>A (p.Arg86Gln) AND not provided
ClinVar Allele ID
34038
ClinVar RefSeq Alternation Syntax
NM_001362782.2:c.-2G>A
ClinVar RefSeq Alternation Syntax
NM_001085425.3:c.257G>A
ClinVar RefSeq Alternation Syntax
NM_000487.6:c.257G>A
ClinVar RefSeq Alternation Syntax
NM_001085426.3:c.257G>A
ClinVar RefSeq Alternation Syntax
NM_001085427.3:c.257G>A
ClinVar RefSeq Alternation Syntax
NM_001085428.3:c.-2G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-06-13
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000723563
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs