Annotation Detail

Information
Associated Genes
ARSA
Associated Variants
ARSA p.Tyr65Ter (p.Y65*) ( ENST00000216124.10, ENST00000356098.9, ENST00000395619.3, ENST00000395621.7, ENST00000453344.6 )
ARSA p.Tyr65Ter (p.Y65*) ( ENST00000216124.10, ENST00000356098.9, ENST00000395619.3, ENST00000395621.7, ENST00000453344.6 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000487.6(ARSA):c.195del (p.Phe64_Tyr65insTer) AND not provided
ClinVar Allele ID
99028
ClinVar RefSeq Alternation Syntax
NM_001085428.3:c.-34-179del
ClinVar RefSeq Alternation Syntax
NM_001085425.3:c.195del
ClinVar RefSeq Alternation Syntax
NM_001085427.3:c.195del
ClinVar RefSeq Alternation Syntax
NM_000487.6:c.195del
ClinVar RefSeq Alternation Syntax
NM_001085426.3:c.195del
ClinVar RefSeq Alternation Syntax
NM_001362782.2:c.-34-179del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2012-07-10
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000723526
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs