Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Gln57Ter (p.Q57*) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Gln57Ter (p.Q57*) ( ENST00000382844.2, ENST00000382848.5 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_004004.6(GJB2):c.169C>T (p.Gln57Ter) AND not provided
ClinVar Allele ID
53892
ClinVar RefSeq Alternation Syntax
NM_004004.6:c.169C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-12-26
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000711347
ClinVar Disease
not provided
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs