Annotation Detail

Information
Associated Genes
VHL LOC107303340
Associated Variants
VHL p.His115Pro (p.H115P) ( ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1, ENST00000256474.3, ENST00000345392.3 )
VHL p.His115Pro (p.H115P) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000551.4(VHL):c.344A>C (p.His115Pro) AND not provided
ClinVar Allele ID
551819
ClinVar RefSeq Alternation Syntax
NM_198156.3:c.341-3270A>C
ClinVar RefSeq Alternation Syntax
NM_000551.4:c.344A>C
ClinVar RefSeq Alternation Syntax
NM_001354723.2:c.*18-3270A>C
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2015-09-16
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000679034
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs