Annotation Detail

Information
Associated Genes
SMPD1
Associated Variants
SMPD1 p.Gly247Ser (p.G247S) ( ENST00000342245.9, ENST00000527275.5 )
SMPD1 p.Gly247Ser (p.G247S) ( ENST00000342245.9, ENST00000527275.5 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000543.5(SMPD1):c.739G>A (p.Gly247Ser) AND not provided
ClinVar Allele ID
106596
ClinVar RefSeq Alternation Syntax
NM_001007593.3:c.736G>A
ClinVar RefSeq Alternation Syntax
NR_027400.3:n.864G>A
ClinVar RefSeq Alternation Syntax
NM_001318088.2:c.-223G>A
ClinVar RefSeq Alternation Syntax
NM_001365135.2:c.739G>A
ClinVar RefSeq Alternation Syntax
NM_001318087.2:c.739G>A
ClinVar RefSeq Alternation Syntax
NM_000543.5:c.739G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-09-10
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000594578
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs