Annotation Detail

Information
Associated Genes
TSC2
Associated Variants
TSC2 p.His1746_Arg1751del (p.H1746_R1751del) ( ENST00000644329.1, ENST00000642797.1, ENST00000350773.9, ENST00000644043.1, ENST00000382538.10, ENST00000439673.6, ENST00000642365.2, ENST00000646388.1, ENST00000642561.1, ENST00000643088.1, ENST00000401874.7, ENST00000568454.6, ENST00000643946.1, ENST00000642206.2, ENST00000644335.1, ENST00000642936.1, ENST00000219476.9, ENST00000645186.2 )
TSC2 p.His1746_Arg1751del (p.H1746_R1751del) ( ENST00000219476.9, ENST00000350773.9, ENST00000382538.10, ENST00000401874.7, ENST00000439673.6, ENST00000568454.6, ENST00000642206.2, ENST00000642365.2, ENST00000642561.1, ENST00000642797.1, ENST00000642936.1, ENST00000643088.1, ENST00000643946.1, ENST00000644043.1, ENST00000644329.1, ENST00000644335.1, ENST00000645186.2, ENST00000646388.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000548.5(TSC2):c.5238_5255del (p.His1746_Arg1751del) AND not provided
ClinVar Allele ID
27441
ClinVar RefSeq Alternation Syntax
NM_001318831.2:c.4506_4523del
ClinVar RefSeq Alternation Syntax
NM_001318829.2:c.4893_4910del
ClinVar RefSeq Alternation Syntax
NM_001370405.1:c.5097_5114del
ClinVar RefSeq Alternation Syntax
NM_021055.3:c.5109_5126del
ClinVar RefSeq Alternation Syntax
NM_000548.5:c.5238_5255del
ClinVar RefSeq Alternation Syntax
NM_001318827.2:c.4929_4946del
ClinVar RefSeq Alternation Syntax
NM_001318832.2:c.5070_5087del
ClinVar RefSeq Alternation Syntax
NM_001363528.2:c.5040_5057del
ClinVar RefSeq Alternation Syntax
NM_001370404.1:c.5106_5123del
ClinVar RefSeq Alternation Syntax
NM_001114382.3:c.5169_5186del
ClinVar RefSeq Alternation Syntax
NM_001077183.3:c.5037_5054del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-08-14
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000483802
ClinVar Disease
not provided
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs