Annotation Detail

Information
Associated Genes
MUTYH
Associated Variants
MUTYH p.Ala31ProfsTer24 (p.A31Pfs*24), ENSG00000288208 p.Ala199ProfsTer27 (p.A199Pfs*27) ( ENST00000710952.2, ENST00000713750.1, ENST00000372110.7, ENST00000531105.5, ENST00000672818.3, ENST00000372098.7, ENST00000448481.5, ENST00000529892.6, ENST00000713751.1, ENST00000488731.6, ENST00000372115.7, ENST00000529984.5, ENST00000354383.10, ENST00000456914.7, ENST00000483127.2, ENST00000672314.2, ENST00000412971.6, ENST00000528013.6, ENST00000372104.5, ENST00000355498.6 )
MUTYH p.Ala31ProfsTer24 (p.A31Pfs*24), ENSG00000288208 p.Ala199ProfsTer27 (p.A199Pfs*27) ( ENST00000354383.10, ENST00000355498.6, ENST00000372098.7, ENST00000372104.5, ENST00000372110.7, ENST00000372115.7, ENST00000412971.6, ENST00000448481.5, ENST00000456914.7, ENST00000483127.2, ENST00000488731.6, ENST00000528013.6, ENST00000529892.6, ENST00000529984.5, ENST00000531105.5, ENST00000672314.2, ENST00000672818.3, ENST00000710952.2, ENST00000713750.1, ENST00000713751.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_001048174.2(MUTYH):c.49del (p.Ala17fs) AND not provided
ClinVar Allele ID
151093
ClinVar RefSeq Alternation Syntax
NM_001293196.2:c.-164del
ClinVar RefSeq Alternation Syntax
NM_001048172.2:c.49del
ClinVar RefSeq Alternation Syntax
NM_001293195.2:c.49del
ClinVar RefSeq Alternation Syntax
NR_146882.2:n.277del
ClinVar RefSeq Alternation Syntax
NM_001048174.2:c.49del
ClinVar RefSeq Alternation Syntax
NM_001048171.2:c.49del
ClinVar RefSeq Alternation Syntax
NM_001128425.2:c.91del
ClinVar RefSeq Alternation Syntax
NM_001350651.2:c.-159del
ClinVar RefSeq Alternation Syntax
NM_001293191.2:c.49del
ClinVar RefSeq Alternation Syntax
NM_001350650.2:c.-223del
ClinVar RefSeq Alternation Syntax
NR_146883.2:n.200del
ClinVar RefSeq Alternation Syntax
NM_001293192.2:c.-164del
ClinVar RefSeq Alternation Syntax
NM_012222.3:c.91del
ClinVar RefSeq Alternation Syntax
NM_001048173.2:c.49del
ClinVar RefSeq Alternation Syntax
NM_001293190.2:c.91del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-07-19
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000479390
ClinVar Disease
not provided
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs