Annotation Detail

Information
Associated Genes
KCNH2
Associated Variants
KCNH2 p.Leu552Ser (p.L552S) ( ENST00000262186.10, ENST00000330883.9, ENST00000713701.1, ENST00000713710.1 )
KCNH2 p.Leu552Ser (p.L552S) ( ENST00000262186.10, ENST00000330883.9, ENST00000713701.1, ENST00000713710.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000238.4(KCNH2):c.1655T>C (p.Leu552Ser) AND not provided
ClinVar Allele ID
78121
ClinVar RefSeq Alternation Syntax
NM_000238.4:c.1655T>C
ClinVar RefSeq Alternation Syntax
NM_001204798.2:c.635T>C
ClinVar RefSeq Alternation Syntax
NM_001406755.1:c.1478T>C
ClinVar RefSeq Alternation Syntax
NM_001406757.1:c.1355T>C
ClinVar RefSeq Alternation Syntax
NM_172057.3:c.635T>C
ClinVar RefSeq Alternation Syntax
NM_001406756.1:c.1367T>C
ClinVar RefSeq Alternation Syntax
NM_172056.3:c.1655T>C
ClinVar RefSeq Alternation Syntax
NM_001406753.1:c.1367T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-09-29
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000223726
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs