Annotation Detail

Information
Associated Genes
KIT
Associated Variants
KIT p.Trp558_Lys559del (p.W558_K559del) ( ENST00000288135.6, ENST00000412167.7, ENST00000686011.1, ENST00000687295.1, ENST00000689832.1, ENST00000689994.1, ENST00000690543.1, ENST00000692783.1, ENST00000687109.1, ENST00000687246.1 )
KIT p.Trp558_Lys559del (p.W558_K559del) ( ENST00000288135.6, ENST00000412167.7, ENST00000686011.1, ENST00000687109.1, ENST00000687246.1, ENST00000687295.1, ENST00000689832.1, ENST00000689994.1, ENST00000690543.1, ENST00000692783.1 )
Associated Disease
gastrointestinal stromal tumor
Source Database
ClinVar
Description
NM_000222.3(KIT):c.1669_1674del (p.Trp557_Lys558del) AND Gastrointestinal stromal tumor
ClinVar Allele ID
224676
ClinVar RefSeq Alternation Syntax
NM_001093772.2:c.1657_1662del
ClinVar RefSeq Alternation Syntax
NM_001385292.1:c.1660_1665del
ClinVar RefSeq Alternation Syntax
NM_001385284.1:c.1672_1677del
ClinVar RefSeq Alternation Syntax
NM_001385286.1:c.1657_1662del
ClinVar RefSeq Alternation Syntax
NM_001385290.1:c.1672_1677del
ClinVar RefSeq Alternation Syntax
NM_001385285.1:c.1669_1674del
ClinVar RefSeq Alternation Syntax
NM_001385288.1:c.1660_1665del
ClinVar RefSeq Alternation Syntax
NM_000222.3:c.1669_1674del
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2016-02-25
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000208566
ClinVar Disease
Gastrointestinal stromal tumor
Observed Origin Sample
unknown
Drugs