Annotation Detail

Information
Associated Genes
SPG7
Associated Variants
SPG7 p.Ala510Val (p.A510V) ( ENST00000644781.1, ENST00000645818.2, ENST00000645897.1, ENST00000646716.1, ENST00000647079.1, ENST00000643649.1, ENST00000646303.1, ENST00000268704.7, ENST00000645063.1 )
SPG7 p.Ala510Val (p.A510V) ( ENST00000268704.7, ENST00000643649.1, ENST00000644781.1, ENST00000645063.1, ENST00000645818.2, ENST00000645897.1, ENST00000646303.1, ENST00000646716.1, ENST00000647079.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_003119.4(SPG7):c.1529C>T (p.Ala510Val) AND not provided
ClinVar Allele ID
51184
ClinVar RefSeq Alternation Syntax
NM_003119.4:c.1529C>T
ClinVar RefSeq Alternation Syntax
NM_001363850.1:c.1529C>T
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2024-03-01
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000195683
ClinVar Disease
not provided
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs