Annotation Detail

Information
Associated Genes
KCNQ1
Associated Variants
KCNQ1 p.Gly269Val (p.G269V) ( ENST00000646564.2, ENST00000335475.6, ENST00000713725.1, ENST00000155840.12, ENST00000496887.7 )
KCNQ1 p.Gly269Val (p.G269V) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000218.3(KCNQ1):c.806G>T (p.Gly269Val) AND not provided
ClinVar Allele ID
197446
ClinVar RefSeq Alternation Syntax
NM_000218.3:c.806G>T
ClinVar RefSeq Alternation Syntax
NM_001406837.1:c.536G>T
ClinVar RefSeq Alternation Syntax
NM_001406836.1:c.806G>T
ClinVar RefSeq Alternation Syntax
NM_181798.2:c.425G>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-10-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000182307
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs