Annotation Detail

Information
Associated Genes
KCNH2
Associated Variants
KCNH2 p.Gly306Trp (p.G306W) ( ENST00000262186.10, ENST00000713701.1, ENST00000713710.1 )
KCNH2 p.Gly306Trp (p.G306W) ( ENST00000262186.10, ENST00000713701.1, ENST00000713710.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000238.4(KCNH2):c.916G>T (p.Gly306Trp) AND not provided
ClinVar Allele ID
78440
ClinVar RefSeq Alternation Syntax
NM_001406757.1:c.616G>T
ClinVar RefSeq Alternation Syntax
NM_172056.3:c.916G>T
ClinVar RefSeq Alternation Syntax
NM_001406756.1:c.628G>T
ClinVar RefSeq Alternation Syntax
NM_001406755.1:c.739G>T
ClinVar RefSeq Alternation Syntax
NM_001406753.1:c.628G>T
ClinVar RefSeq Alternation Syntax
NM_000238.4:c.916G>T
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2016-06-10
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000182020
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs