Annotation Detail

Information
Associated Genes
KCNH2
Associated Variants
KCNH2 p.Val822Leu (p.V822L) ( ENST00000262186.10, ENST00000330883.9, ENST00000713701.1, ENST00000713710.1 )
KCNH2 p.Val822Leu (p.V822L) ( ENST00000262186.10, ENST00000330883.9, ENST00000713701.1, ENST00000713710.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000238.4(KCNH2):c.2464G>C (p.Val822Leu) AND not provided
ClinVar Allele ID
197199
ClinVar RefSeq Alternation Syntax
NM_001406753.1:c.2176G>C
ClinVar RefSeq Alternation Syntax
NM_172057.3:c.1444G>C
ClinVar RefSeq Alternation Syntax
NR_176254.1:n.2872G>C
ClinVar RefSeq Alternation Syntax
NM_000238.4:c.2464G>C
ClinVar RefSeq Alternation Syntax
NR_176255.1:n.1745G>C
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2017-06-15
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000181866
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs